Congenital perineal grove: an unusual Anorectal anomaly in females—report of two cases and literature review Authors Bakhtawar Dilawar Department of Paediatrics Surgery, Aga Khan University Hospital, Karachi, Pakistan Amala Khan Department of Paediatrics, Aga Khan University Hospital, Karachi, Pakistan Shahzadi Dilawar Department of Paediatrics, National Institute of Child and Health Science, Karachi, Pakistan Zafar Nazir Department of Paediatrics Surgery, Aga Khan University Hospital, Karachi, Pakistan DOI: https://doi.org/10.47391/JPMA.6803 Keywords: Anorectal malformations, Perineal cleft, Perineal grove Abstract Congenital perineal grove (CPG) is a rare anorectal anomaly; only 65 cases have been reported in literature. Two cases who were referred for evaluation of a lesion in the perineum are reported here. The patients were diagnosed clinically as CPG in neonatal period and were initially managed conservatively. Surgery was required in one case as the lesion was persistent and symptomatic. A high index of suspicion is required for diagnosis of CPG to avoid parental anxiety and unnecessary diagnostic work-up and surgery. Surgery is required only in cases where the lesion persists or there is infection, pain, and ulceration. Keywords: Anorectal malformations, Perineal cleft, Perineal grove. Downloads Full Text Article Published 2023-05-15 How to Cite Dilawar, B., Khan, A., Shahzadi Dilawar, & Zafar Nazir. (2023). Congenital perineal grove: an unusual Anorectal anomaly in females—report of two cases and literature review. Journal of the Pakistan Medical Association, 73(6), 1311–1313. https://doi.org/10.47391/JPMA.6803 More Citation Formats ACM ACS APA ABNT Chicago Harvard IEEE MLA Turabian Vancouver Download Citation Endnote/Zotero/Mendeley (RIS) BibTeX Issue Vol. 73 No. 6 (2023): JUNE Section CASE REPORT License Copyright (c) 2020 Journal of the Pakistan Medical Association This work is licensed under a Creative Commons Attribution 4.0 International License.